Langerhans Cell Histiocytosis (LCH) Presenting as Decompensated Liver Disease: Case Report

Chhagan Bihari, Archana Rastogi, Apurba Rajbongshi, Vikrant Sood, Rajeev Khanna, Seema Alam

Abstract


Langerhans’cell histiocytosis (LCH) is a rare disease characterized by clonal proliferation of Langerhans cells. It manifests as single system unifocal, multifocal or multisystem disease. The diagnosis is always on histological assessment. We report a case of Langerhans’ cell histiocytosis in a young child with clinical signs of decompensated liver disease whom the histological and immunohistochemical analysis of the liver biopsy, lymph node biopsy and radiology formed the diagnosis of multisystemic LCH.

Keywords


LCH; Decompensated liver disease; Sclerosing cholangitis

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